Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature

Detalhes bibliográficos
Autor(a) principal: Barbosa, NC
Data de Publicação: 2020
Outros Autores: Ramos, A, Sagarribay, A, Ribeiro, MJ
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10400.17/4693
Resumo: We present a case study of a 5-year-old patient, who presented with left-sided torticollis. Due to persistence of problems, a CT and an MRI were made showing a single osteolytic lesion centred on right occipital condyle. After an open biopsy, histology confirmed it to be Langerhans cell histiocytosis (LCH). Torticollis or restricted range of motion is a presenting feature in 76% of children with LCH with cervical involvement. There remains much debate on the best treatment strategy. The clinical and radiological outcomes of the case study presented on this article support the treatment of LCH with chemotherapy in cases with solitary involvement of the occipital condyle.
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spelling Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the LiteratureChild, PreschoolHistiocytosis, Langerhans-Cell / complicationsHistiocytosis, Langerhans-Cell / diagnosisHistiocytosis, Langerhans-Cell / surgeryMagnetic Resonance ImagingNeck Pain / etiologyOccipital Bone / diagnostic imagingOccipital Bone / pathology*Occipital Bone / surgeryRadionuclide ImagingTomography, X-Ray ComputedTorticollis / etiologyHDE NCIRWe present a case study of a 5-year-old patient, who presented with left-sided torticollis. Due to persistence of problems, a CT and an MRI were made showing a single osteolytic lesion centred on right occipital condyle. After an open biopsy, histology confirmed it to be Langerhans cell histiocytosis (LCH). Torticollis or restricted range of motion is a presenting feature in 76% of children with LCH with cervical involvement. There remains much debate on the best treatment strategy. The clinical and radiological outcomes of the case study presented on this article support the treatment of LCH with chemotherapy in cases with solitary involvement of the occipital condyle.BMJRepositório do Centro Hospitalar Universitário de Lisboa Central, EPEBarbosa, NCRamos, ASagarribay, ARibeiro, MJ2023-09-11T12:18:52Z20202020-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/4693engBMJ Case Rep . 2020 Dec 12;13(12):e23563010.1136/bcr-2020-235630info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-09-17T06:26:50Zoai:repositorio.chlc.min-saude.pt:10400.17/4693Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T20:29:29.367559Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
title Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
spellingShingle Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
Barbosa, NC
Child, Preschool
Histiocytosis, Langerhans-Cell / complications
Histiocytosis, Langerhans-Cell / diagnosis
Histiocytosis, Langerhans-Cell / surgery
Magnetic Resonance Imaging
Neck Pain / etiology
Occipital Bone / diagnostic imaging
Occipital Bone / pathology*
Occipital Bone / surgery
Radionuclide Imaging
Tomography, X-Ray Computed
Torticollis / etiology
HDE NCIR
title_short Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
title_full Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
title_fullStr Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
title_full_unstemmed Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
title_sort Langerhans Cell Histiocytosis in the Occipital Condyle: A Case Study and a Brief Review of the Literature
author Barbosa, NC
author_facet Barbosa, NC
Ramos, A
Sagarribay, A
Ribeiro, MJ
author_role author
author2 Ramos, A
Sagarribay, A
Ribeiro, MJ
author2_role author
author
author
dc.contributor.none.fl_str_mv Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE
dc.contributor.author.fl_str_mv Barbosa, NC
Ramos, A
Sagarribay, A
Ribeiro, MJ
dc.subject.por.fl_str_mv Child, Preschool
Histiocytosis, Langerhans-Cell / complications
Histiocytosis, Langerhans-Cell / diagnosis
Histiocytosis, Langerhans-Cell / surgery
Magnetic Resonance Imaging
Neck Pain / etiology
Occipital Bone / diagnostic imaging
Occipital Bone / pathology*
Occipital Bone / surgery
Radionuclide Imaging
Tomography, X-Ray Computed
Torticollis / etiology
HDE NCIR
topic Child, Preschool
Histiocytosis, Langerhans-Cell / complications
Histiocytosis, Langerhans-Cell / diagnosis
Histiocytosis, Langerhans-Cell / surgery
Magnetic Resonance Imaging
Neck Pain / etiology
Occipital Bone / diagnostic imaging
Occipital Bone / pathology*
Occipital Bone / surgery
Radionuclide Imaging
Tomography, X-Ray Computed
Torticollis / etiology
HDE NCIR
description We present a case study of a 5-year-old patient, who presented with left-sided torticollis. Due to persistence of problems, a CT and an MRI were made showing a single osteolytic lesion centred on right occipital condyle. After an open biopsy, histology confirmed it to be Langerhans cell histiocytosis (LCH). Torticollis or restricted range of motion is a presenting feature in 76% of children with LCH with cervical involvement. There remains much debate on the best treatment strategy. The clinical and radiological outcomes of the case study presented on this article support the treatment of LCH with chemotherapy in cases with solitary involvement of the occipital condyle.
publishDate 2020
dc.date.none.fl_str_mv 2020
2020-01-01T00:00:00Z
2023-09-11T12:18:52Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/4693
url http://hdl.handle.net/10400.17/4693
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv BMJ Case Rep . 2020 Dec 12;13(12):e235630
10.1136/bcr-2020-235630
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv BMJ
publisher.none.fl_str_mv BMJ
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
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reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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