A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report

Detalhes bibliográficos
Autor(a) principal: Bittencourt, Achilea Candida Lisboa
Data de Publicação: 2009
Outros Autores: Mota, Karla, Oliveira, Rodrigo Freire, Farré, Lourdes
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UFBA
Texto Completo: http://repositorio.ufba.br/ri/handle/ri/13808
Resumo: Texto completo: acesso restrito. p. 834-837
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spelling Bittencourt, Achilea Candida LisboaMota, KarlaOliveira, Rodrigo FreireFarré, LourdesBittencourt, Achilea Candida LisboaMota, KarlaOliveira, Rodrigo FreireFarré, Lourdes2013-11-19T20:56:59Z20090193-1091http://repositorio.ufba.br/ri/handle/ri/13808v. 31, n. 8Texto completo: acesso restrito. p. 834-837Adult T-cell leukemia/lymphoma (ATL) is an aggressive type of leukemia/lymphoma associated with the human T-cell lymphotropic virus (HTLV-I). We describe an adult male patient clinically and pathologically diagnosed as mycosis fungoides and treated with chemotherapy after which complete involution of the lesions occurred. The disease relapsed with confluent dyshidrosis-like vesicles on the palmoplantar regions, followed by disseminated vesiculopapules and associated lymphocytosis. A serological test performed at this time revealed HTLV-I infection, and a diagnosis of chronic ATL was made. Monoclonal integration of HTLV-I was detected in peripheral blood mononuclear cells by inverse long polymerase chain reaction. A skin biopsy revealed spongiosis, Pautrier abscesses, and intraepidermal vesicles with atypical lymphocytes and an infiltration of small and atypical CD4+ lymphocytes in the superficial dermis. Proliferative index (Ki-67) was 70%. This is the first reported vesicular cutaneous ATL with confirmation of HTLV-I proviral integration. The delay that occurred in diagnosing ATL was due to the fact that mycosis fungoides and ATL may present the same clinical, histopathological, and immunohistochemical features.Submitted by Suelen Reis (suziy.ellen@gmail.com) on 2013-09-24T11:58:34Z No. of bitstreams: 1 00000372-200912000-00021.pdf: 1048576 bytes, checksum: 60876c29d856bc0e55a3f8fb4787a989 (MD5)Approved for entry into archive by Rodrigo Meirelles (rodrigomei@ufba.br) on 2013-11-19T20:56:59Z (GMT) No. of bitstreams: 1 00000372-200912000-00021.pdf: 1048576 bytes, checksum: 60876c29d856bc0e55a3f8fb4787a989 (MD5)Made available in DSpace on 2013-11-19T20:56:59Z (GMT). No. of bitstreams: 1 00000372-200912000-00021.pdf: 1048576 bytes, checksum: 60876c29d856bc0e55a3f8fb4787a989 (MD5) Previous issue date: 2009http://dx.doi.org/10.1097/DAD.0b013e3181ac04fereponame:Repositório Institucional da UFBAinstname:Universidade Federal da Bahia (UFBA)instacron:UFBAAdult T-cell leukemia/lymphomaMycosis fungoidesHTLV-I infectionA dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. 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dc.title.pt_BR.fl_str_mv A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
dc.title.alternative.pt_BR.fl_str_mv American Journal of Dermatopathology
title A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
spellingShingle A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
Bittencourt, Achilea Candida Lisboa
Adult T-cell leukemia/lymphoma
Mycosis fungoides
HTLV-I infection
title_short A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
title_full A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
title_fullStr A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
title_full_unstemmed A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
title_sort A dyshidrosis-like variant of adult T-cell leukemia/lymphoma with clinicopathological aspects of mycosis fungoides. A case report
author Bittencourt, Achilea Candida Lisboa
author_facet Bittencourt, Achilea Candida Lisboa
Mota, Karla
Oliveira, Rodrigo Freire
Farré, Lourdes
author_role author
author2 Mota, Karla
Oliveira, Rodrigo Freire
Farré, Lourdes
author2_role author
author
author
dc.contributor.author.fl_str_mv Bittencourt, Achilea Candida Lisboa
Mota, Karla
Oliveira, Rodrigo Freire
Farré, Lourdes
Bittencourt, Achilea Candida Lisboa
Mota, Karla
Oliveira, Rodrigo Freire
Farré, Lourdes
dc.subject.por.fl_str_mv Adult T-cell leukemia/lymphoma
Mycosis fungoides
HTLV-I infection
topic Adult T-cell leukemia/lymphoma
Mycosis fungoides
HTLV-I infection
description Texto completo: acesso restrito. p. 834-837
publishDate 2009
dc.date.issued.fl_str_mv 2009
dc.date.accessioned.fl_str_mv 2013-11-19T20:56:59Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv http://repositorio.ufba.br/ri/handle/ri/13808
dc.identifier.issn.none.fl_str_mv 0193-1091
dc.identifier.number.pt_BR.fl_str_mv v. 31, n. 8
identifier_str_mv 0193-1091
v. 31, n. 8
url http://repositorio.ufba.br/ri/handle/ri/13808
dc.language.iso.fl_str_mv eng
language eng
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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